{"id":140,"date":"2023-08-08T18:07:32","date_gmt":"2023-08-08T21:07:32","guid":{"rendered":"https:\/\/adm.org.ar\/newsite\/?page_id=140"},"modified":"2023-08-08T18:08:31","modified_gmt":"2023-08-08T21:08:31","slug":"las-distrofias-musculares","status":"publish","type":"page","link":"https:\/\/adm.org.ar\/newsite\/las-distrofias-musculares\/","title":{"rendered":"Las Distrofias Musculares"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"140\" class=\"elementor elementor-140\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5d9c01a elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5d9c01a\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-ed55afa\" data-id=\"ed55afa\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-10f5294 elementor-widget elementor-widget-heading\" data-id=\"10f5294\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Las Distrofias Musculares<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-d9062c4 elementor-widget elementor-widget-text-editor\" data-id=\"d9062c4\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Las distrofias musculares se refieren a un grupo de m\u00e1s de 100 enfermedades neuromusculares de origen gen\u00e9tico que causan debilidad y degeneraci\u00f3n progresiva de los m\u00fasculos.\u00a0<\/p><p>Las diferentes formas de Distrofia Muscular var\u00edan en la edad de inicio de los s\u00edntomas, gravedad, y patr\u00f3n de m\u00fasculos afectados. Todas las formas de distrofia muscular progresan a medida que los m\u00fasculos degeneran y se debilitan. Dependiendo del tipo y evoluci\u00f3n muchas de ellas conducen a la discapacidad y las personas pueden perder la capacidad de caminar.<\/p><p>Algunos tipos de distrofia muscular tambi\u00e9n afectan al m\u00fasculo card\u00edaco y los\u00a0 m\u00fasculos necesarios para la respiraci\u00f3n por lo que pueden conducir a la insuficiencia cardiaca y \/o respiratoria.\u00a0<\/p><p>Los m\u00fasculos encargados de la degluci\u00f3n o la fonaci\u00f3n as\u00ed como los m\u00fasculos encargados de mover los globos oculares pueden hallarse involucrados en algunas formas de DM.\u00a0<\/p><ul><li aria-level=\"1\"><b>\u00bfCu\u00e1les son las causas?<\/b><\/li><\/ul><p>Las distrofias musculares son de origen gen\u00e9tico, es decir son causadas por un defecto en los genes, que son los encargados de dirigir la producci\u00f3n de prote\u00ednas que componen las c\u00e9lulas (en este caso, musculares) y son necesarias para funciones indispensables de su vida.<\/p><p>En las distrofias musculares una anormalidad en una prote\u00edna causa que los m\u00fasculos se debiliten y atrofien. Las c\u00e9lulas musculares Imposibilitadas de\u00a0 funcionar correctamente por la anormalidad proteica mueren y son reemplazadas por grasa y tejido conectivo.<\/p><ul><li aria-level=\"1\"><b>\u00bfQu\u00e9 forma de herencia tienen?<\/b><\/li><\/ul><p>Existen distintos tipos de herencia dependiendo de la enfermedad que se trate: autos\u00f3mica dominante, autos\u00f3mica recesiva y recesiva ligada al sexo. Es importante adem\u00e1s aclarar que muchas formas de distrofia muscular tambi\u00e9n pueden ser el resultado de una mutaci\u00f3n nueva, o espont\u00e1nea. En este caso aparece por primera vez en la historia de la familia una enfermedad de este tipo.<\/p><p>En las formas recesivas la enfermedad puede no haberse manifestado previamente en la familia.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Las Distrofias Musculares Las distrofias musculares se refieren a un grupo de m\u00e1s de 100 enfermedades neuromusculares de origen gen\u00e9tico que causan debilidad y degeneraci\u00f3n progresiva de los m\u00fasculos.\u00a0 Las diferentes formas de Distrofia Muscular var\u00edan en la edad de inicio de los s\u00edntomas, gravedad, y patr\u00f3n de m\u00fasculos afectados. Todas las formas de distrofia [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_joinchat":[],"footnotes":""},"class_list":["post-140","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Las Distrofias Musculares - ADM Argentina<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/adm.org.ar\/newsite\/las-distrofias-musculares\/\" \/>\n<meta property=\"og:locale\" content=\"es_ES\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Las Distrofias Musculares - ADM Argentina\" \/>\n<meta property=\"og:description\" content=\"Las Distrofias Musculares Las distrofias musculares se refieren a un grupo de m\u00e1s de 100 enfermedades neuromusculares de origen gen\u00e9tico que causan debilidad y degeneraci\u00f3n progresiva de los m\u00fasculos.\u00a0 Las diferentes formas de Distrofia Muscular var\u00edan en la edad de inicio de los s\u00edntomas, gravedad, y patr\u00f3n de m\u00fasculos afectados. 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